Гнійничкова гангренозна піодермія
ORPHA:538866· ICD-10 L88· Pustular pyoderma gangrenosum
Визначення(English summary)
A rare subtype of pyoderma gangrenosum characterized by multiple painful, sterile pustules with a surrounding erythematous halo, predominantly occurring on the trunk and extensor surfaces of the limbs, and potentially persisting for months. Histopathology shows a dermal neutrophilic infiltrate and subcorneal neutrophilic micropustules. The condition is commonly associated with inflammatory bowel disease.
- Поширеність
- Unknown
- Успадкування
- Multigenic/multifactorial
- Вік початку
- Adolescent, Adult, Childhood, Elderly