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Pustular pyoderma gangrenosum

ORPHA:538866· ICD-10 L88

Definition

A rare subtype of pyoderma gangrenosum characterized by multiple painful, sterile pustules with a surrounding erythematous halo, predominantly occurring on the trunk and extensor surfaces of the limbs, and potentially persisting for months. Histopathology shows a dermal neutrophilic infiltrate and subcorneal neutrophilic micropustules. The condition is commonly associated with inflammatory bowel disease.

Prevalence
Unknown
Inheritance
Multigenic/multifactorial
Age of onset
Adolescent, Adult, Childhood, Elderly