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Псевдо-хвороба Віллебранда

ORPHA:52530· ICD-10 D69.8· Pseudo-von Willebrand disease

Визначення(English summary)

A bleeding disorder characterized by mild to moderate mucocutaneous bleeding, which becomes more pronounced during pregnancy or following ingestion of drugs that have anti-platelet activity. This disease is due to hyperresponsive platelets, resulting in thrombocytopenia.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal dominant
Вік початку
Adult