vitalwiki

Pseudo-von Willebrand disease

ORPHA:52530· ICD-10 D69.8

Definition

A bleeding disorder characterized by mild to moderate mucocutaneous bleeding, which becomes more pronounced during pregnancy or following ingestion of drugs that have anti-platelet activity. This disease is due to hyperresponsive platelets, resulting in thrombocytopenia.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Adult