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Набута фульминантна пурпура

ORPHA:49566· ICD-10 D65· Acquired purpura fulminans

Визначення(English summary)

A life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children that is characterized by purpuric skin lesions and disseminated intravascular coagulation. It may progress rapidly to multi-organ failure caused by thrombotic occlusion of small and medium-sized blood vessels. There are two forms of the disorder that are classified according to triggering mechanisms: acute infectious (the most common form), and idiopathic purpura fulminans.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adult, Childhood, Infancy, Neonatal