Аденокарцинома жовчного міхура та позапечінкових жовчовивідних шляхів
ORPHA:424991· ICD-10 C23· Adenocarcinoma of the gallbladder and extrahepatic biliary tract
Визначення(English summary)
A rare epithelial carcinoma, arising either in the gallbladder itself or from the epithelium lining the extrahepatic biliary tree, cystic duct and/or peribiliary gland, characterized by nonspecific symptoms, such as abdominal pain, jaundice and vomiting and sometimes mimicking benign biliary diseases. Chronic biliary epithelial inflammation (e.g. primary sclerosing cholangitis, cholelithiasis, choledocholithiasis, liver fluke infestation) is a major risk factor.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Not applicable
- Вік початку
- Adult