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Спадковий світлоклітинний рак нирки

ORPHA:422526· ICD-10 C64· Hereditary clear cell renal cell carcinoma

Визначення(English summary)

Hereditary clear cell renal cell carcinoma (ccRCC) is a hereditary renal cancer syndrome defined as development of ccRCC in two or more family members without evidence of constitutional chromosome 3 translocation, von Hippel-Lindau disease or other tumor predisposing syndromes associated with ccRCC, such as tuberous sclerosis or Birt-Hogg-Dubbé syndrome.

Поширеність
Unknown
Успадкування
Unknown
Вік початку
Adult