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Неонатальний антифосфоліпідний синдром

ORPHA:398097· ICD-10 D68.6· Neonatal antiphospholipid syndrome

Визначення(English summary)

Neonatal antiphospholipid syndrome is a rare, secondary, neonatal autoimmune disease characterized by single or recurrent episodes of venous, arterial or mixed thrombosis in a neonate whose mother does not have antiphospholipid syndrome manifestations. Patients present positive antiphospholipid antibodies and may have additional abnormalities associated (e.g. cardiac valve disease, livedo reticularis, thrombocytopenia, nephropathy, neurological manifestations).

Поширеність
<1 / 1 000 000
Вік початку
Neonatal