Неонатальний антифосфоліпідний синдром
ORPHA:398097· ICD-10 D68.6· Neonatal antiphospholipid syndrome
Визначення(English summary)
Neonatal antiphospholipid syndrome is a rare, secondary, neonatal autoimmune disease characterized by single or recurrent episodes of venous, arterial or mixed thrombosis in a neonate whose mother does not have antiphospholipid syndrome manifestations. Patients present positive antiphospholipid antibodies and may have additional abnormalities associated (e.g. cardiac valve disease, livedo reticularis, thrombocytopenia, nephropathy, neurological manifestations).
- Поширеність
- <1 / 1 000 000
- Вік початку
- Neonatal