Саркома Капоші
ORPHA:33276· ICD-10 C46.0· Kaposi sarcoma
Визначення(English summary)
A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.
- Поширеність
- 1-9 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Adult