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Kaposi sarcoma

ORPHA:33276· ICD-10 C46.0

Definition

A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.

Prevalence
1-9 / 1 000 000
Inheritance
Not applicable
Age of onset
Adult