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Аутоімунна поліендокринопатія, тип 2

ORPHA:3143· ICD-10 E31.0· Autoimmune polyendocrinopathy type 2

Визначення(English summary)

A rare, endocrine disease characterized by autoimmune Addison disease associated with autoimmune thyroid disease or type I diabetes mellitus, or both, and without chronic candidiasis. Additional endocrine (hypogonadism, hypoparathyroidism) and non-endocrine diseases (vitiligo, autoimmune hepatitis, autoimmune gastritis, pernicious anemia, and myasthenia gravies) may be present.

Поширеність
Unknown
Вік початку
Adult