Аутоімунна поліендокринопатія, тип 2
ORPHA:3143· ICD-10 E31.0· Autoimmune polyendocrinopathy type 2
Визначення(English summary)
A rare, endocrine disease characterized by autoimmune Addison disease associated with autoimmune thyroid disease or type I diabetes mellitus, or both, and without chronic candidiasis. Additional endocrine (hypogonadism, hypoparathyroidism) and non-endocrine diseases (vitiligo, autoimmune hepatitis, autoimmune gastritis, pernicious anemia, and myasthenia gravies) may be present.
- Поширеність
- Unknown
- Вік початку
- Adult