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Autoimmune polyendocrinopathy type 2

ORPHA:3143· ICD-10 E31.0

Definition

A rare, endocrine disease characterized by autoimmune Addison disease associated with autoimmune thyroid disease or type I diabetes mellitus, or both, and without chronic candidiasis. Additional endocrine (hypogonadism, hypoparathyroidism) and non-endocrine diseases (vitiligo, autoimmune hepatitis, autoimmune gastritis, pernicious anemia, and myasthenia gravies) may be present.

Prevalence
Unknown
Age of onset
Adult