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Ідіопатична нейтропенія у дорослих

ORPHA:2688· ICD-10 D70· Adult idiopathic neutropenia

Визначення(English summary)

A rare acquired immunodeficiency disease characterized by adult-onset absolute neutrophil counts less than 1.5 x 10^9/L on at least 3 occasions in a 3 month period that cannot be attributable to drugs or a specific genetic, infectious, inflammatory, autoimmune or malignant cause. Recurrent aphtous stomatitis and a history of mild bacterial infections are typically associated. A benign outcome with a low rate of severe infections and no secondary malignancies is observed.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adult