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Ізольований пульмонарний капілярит

ORPHA:264691· ICD-10 J84.8· Isolated pulmonary capillaritis

Визначення(English summary)

Isolated pauciimmune pulmonary capillaritis is a small vessel vasculitis restricted to the lungs that may induce diffuse alveolar hemorrhage with dyspnea, anemia, chest pain, hemoptysis, bilateral and diffuse alveolar infiltrates at chest X-rays, without any underlying systemic disease. ANCA are frequently positive but could be negative.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Childhood