Первинна одностороння гіперплазія надниркових залоз
ORPHA:231580· ICD-10 E26.0· Primary unilateral adrenal hyperplasia
Визначення(English summary)
Primary unilateral adrenal hyperplasia (PUAH) is a surgically-correctable form of primary (hyper) aldosteronism (PA; see this term) characterized by renin suppression, unilateral aldosterone hypersecretion, and moderate to severe hypertension secondary to hyperplasia of the adrenal gland.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- All ages