Primary unilateral adrenal hyperplasia
ORPHA:231580· ICD-10 E26.0
Definition
Primary unilateral adrenal hyperplasia (PUAH) is a surgically-correctable form of primary (hyper) aldosteronism (PA) characterized by renin suppression, unilateral aldosterone hypersecretion, and moderate to severe hypertension secondary to hyperplasia of the adrenal gland.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- All ages