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Глотково-шийно-плечовий варіант синдрому Гійєна-Барре

ORPHA:231426· ICD-10 G61.0· Pharyngeal-cervical-brachial variant of Guillain-Barré syndrome

Визначення(English summary)

Pharyngeal-cervical-brachial variant of Guillain-Barré syndrome is a rare, acquired peripheral neuropathy disease characterized by rapidly progressive oropharyngeal (facial palsy, dysarthria) and cervicobrachial weakness, associated with upper limb weakness and hypo/areflexia, in the absence of ophthalmoplegia, ataxia, altered consciousness, and prominent lower limb weakness. The presence of monospecific IgG anti-GT1a antibodies is associated.

Успадкування
Multigenic/multifactorial, Not applicable
Вік початку
All ages