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Pharyngeal-cervical-brachial variant of Guillain-Barré syndrome

ORPHA:231426· ICD-10 G61.0

Definition

Pharyngeal-cervical-brachial variant of Guillain-Barré syndrome is a rare, acquired peripheral neuropathy disease characterized by rapidly progressive oropharyngeal (facial palsy, dysarthria) and cervicobrachial weakness, associated with upper limb weakness and hypo/areflexia, in the absence of ophthalmoplegia, ataxia, altered consciousness, and prominent lower limb weakness. The presence of monospecific IgG anti-GT1a antibodies is associated.

Inheritance
Multigenic/multifactorial, Not applicable
Age of onset
All ages