Синдром ідіопатичного увеального випоту
ORPHA:209956· ICD-10 H31.8· Idiopathic uveal effusion syndrome
Визначення(English summary)
A rare panuveitis characterized by uni- or bilateral abnormal fluid accumulation within the suprachoroidal space, resulting in internal choroidal elevation, in the absence of any known cause, such as decreased intraocular tension, intraocular tumor, intraocular inflammation or nanophtalmos. Patients typically present a protracted, relapsing-remitting course of visual acuity loss and fundus examination shows annular celio-choroidal detachment and shifting, serous retinal detachment.
- Поширеність
- Unknown
- Успадкування
- Unknown
- Вік початку
- Adult