vitalwiki

Idiopathic uveal effusion syndrome

ORPHA:209956· ICD-10 H31.8

Definition

A rare panuveitis characterized by uni- or bilateral abnormal fluid accumulation within the suprachoroidal space, resulting in internal choroidal elevation, in the absence of any known cause, such as decreased intraocular tension, intraocular tumor, intraocular inflammation or nanophtalmos. Patients typically present a protracted, relapsing-remitting course of visual acuity loss and fundus examination shows annular celio-choroidal detachment and shifting, serous retinal detachment.

Prevalence
Unknown
Inheritance
Unknown
Age of onset
Adult