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Вульвовагінальна рабдоміосаркома

ORPHA:206492· ICD-10 C52· Vulvovaginal rhabdomyosarcoma

Визначення(English summary)

Vulvovaginal rhabdomyosarcoma is a rare vulvovaginal tumour, a highly malignant soft tissue sarcoma composed of cells with round to oval or spindle-shaped nuclei and eosinophilic cytoplasm that may show differentiation towards striated muscle cells. It usually affects children and presents with a vulvar or vaginal mass that may be polypoid or grape-like (embryonal subtype) and associated with bleeding and ulceration.