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Синдром Еванса

ORPHA:1959· ICD-10 D69.3· Evans syndrome

Визначення(English summary)

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Поширеність
1-9 / 1 000 000
Успадкування
Not applicable
Вік початку
Adult, Childhood