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Первинна шкірна лімфома фолікулярного центру

ORPHA:178540· ICD-10 C82.6· Primary cutaneous follicle center lymphoma

Визначення(English summary)

A rare, indolent primary cutaneous B-cell lymphoma characterized by a solitary or grouped erythematous plaques or tumors, preferentially located on the head, neck or trunk region, and composed of centroblasts and centrocytes arranged in a follicular, diffuse, or mixed growth pattern. The lesions are smooth and typically do not ulcerate. The neoplastic cells express pan B cell markers and Bcl-6, and typically lack Bcl-2.