Локалізований пагетоїдний ретикулоз
ORPHA:178517· ICD-10 C84.0· Localized pagetoid reticulosis
Визначення(English summary)
A rare variant of mycosis fungoides (MF), a form of cutaneous T-cell lymphoma, characterized by the presence of localized patches or plaques with epidermal hyperplasia and intraepidermal proliferation of neoplastic T-cells, usually involving one extremity.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- Adult