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Локалізований пагетоїдний ретикулоз

ORPHA:178517· ICD-10 C84.0· Localized pagetoid reticulosis

Визначення(English summary)

A rare variant of mycosis fungoides (MF), a form of cutaneous T-cell lymphoma, characterized by the presence of localized patches or plaques with epidermal hyperplasia and intraepidermal proliferation of neoplastic T-cells, usually involving one extremity.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adult