Localized pagetoid reticulosis
ORPHA:178517· ICD-10 C84.0
Definition
A rare variant of mycosis fungoides (MF), a form of cutaneous T-cell lymphoma, characterized by the presence of localized patches or plaques with epidermal hyperplasia and intraepidermal proliferation of neoplastic T-cells, usually involving one extremity.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- Adult