Дефіцит аргінін-вазопресину
ORPHA:178029· ICD-10 E23.2· Arginine vasopressin deficiency
Визначення(English summary)
Central diabetes insipidus (CDI) is a hypothalamus-pituitary disease characterized by polyuria and polydipsia due to a vasopressin (AVP) deficiency. It can be inherited or acquired (hereditary CDI and acquired CDI; see these terms).
- Поширеність
- 1-9 / 100 000
- Успадкування
- Autosomal dominant, Autosomal recessive, X-linked dominant
- Вік початку
- Childhood