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Arginine vasopressin deficiency

ORPHA:178029· ICD-10 E23.2

Definition

Central diabetes insipidus (CDI) is a hypothalamus-pituitary disease characterized by polyuria and polydipsia due to a vasopressin (AVP) deficiency. It can be inherited or acquired (hereditary CDI and acquired CDI).

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant, Autosomal recessive, X-linked dominant
Age of onset
Childhood