Герпетиформний дерматит
ORPHA:1656· ICD-10 L13.0· Dermatitis herpetiformis
Визначення(English summary)
A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance.
- Поширеність
- 1-5 / 10 000
- Успадкування
- Not applicable
- Вік початку
- All ages