Dermatitis herpetiformis
ORPHA:1656· ICD-10 L13.0
Definition
A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Not applicable
- Age of onset
- All ages