Криптогенні пізні епілептичні спазми
ORPHA:163708· ICD-10 G40.4· Cryptogenic late-onset epileptic spasms
Визначення(English summary)
Cryptogenic late-onset epileptic spasms is a rare epilepsy syndrome characterized by late-onset (after 1 year old) epileptic spasms that ocurr in clusters, associated with tonic seizures, atypical absences and cognitive deterioration. Language difficulties and behavior problems are frequently present. EEG is characterized by a temporal, or temporofrontal, slow wave or spike focus combined with synchronous spike-waves and no hypsarrhythmia or background activity.
- Поширеність
- Unknown
- Вік початку
- Childhood