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Дисплазія Грінберга

ORPHA:1426· ICD-10 Q77.3· Greenberg dysplasia

Визначення(English summary)

Greenberg dysplasia is a very rare lethal skeletal dysplasia characterized by fetal hydrops, short limbs and abnormal chondro-osseous calcification. The disease is characterized by early in utero lethality and affected fetuses are considered as nonviable.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal recessive
Вік початку
Antenatal, Neonatal