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Colobomatous microphthalmia

ORPHA:98938· ICD-10 Q11.2

Definition

Colobomatous microphthalmia is a developmental disorder of the eye characterized by unilateral or bilateral microphthalmia associated with ocular coloboma.

Prevalence
1-5 / 10 000
Inheritance
Autosomal dominant, Autosomal recessive
Age of onset
Antenatal, Neonatal