Congenital megacalycosis
ORPHA:93109· ICD-10 Q63.8
Definition
Congenital megacalycosis is a rare renal malformation, characterized by non-obstructive dilation of the renal calyces as well as an increased calyceal number (12-20), with a normal renal pelvis, ureter, and bladder. It may be unilateral or bilateral and is usually asymptomatic unless complicated by nephrolithiasis and urinary tract infection.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Unknown
- Age of onset
- All ages