vitalwiki

Wild type ABeta2M amyloidosis

ORPHA:85446· ICD-10 E85.3

Definition

A form of amyloidosis affecting patients with chronic kidney disease (CKD), on long term dialysis characterized by the accumulation of amyloid fibrils consisting of beta 2 microglobulin (β2M) deposits in the musculoskeletal system leading to carpal tunnel syndrome (CTS), chronic arthropathy, cystic bone lesions, destructive osteoarthropathy, and pathologic fractures.

Prevalence
1-9 / 100 000
Inheritance
Not applicable
Age of onset
Adult