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3-methylglutaconic aciduria type 4

ORPHA:67048· ICD-10 E71.1

Definition

3-methylglutaconic aciduria (3-MGA) type IV, or unclassified 3-MGA, is a clinically heterogeneous disorder characterised by increased 3-methylglutaconic acid excretion in individuals that cannot be classified as having one of the other forms of 3-MGA (3-MGA I, II or III).

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal