Dentinogenesis imperfecta
ORPHA:49042· ICD-10 K00.5
Definition
Dentinogenesis imperfecta (DGI) is a hereditary dentin defect characterized by abnormal dentin structure resulting in abnormal tooth development.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Autosomal dominant
- Age of onset
- Childhood