Familial hyperaldosteronism type II
ORPHA:404· ICD-10 E26.0
Definition
A heritable form of primary aldosteronism (PA) characterized by hypertension of varying severity, non-glucocorticoid remediable hyperaldosteronism, variable hypokalemia, low plasma renin activity (PRA) and increased aldosterone-to-renin ratio.
- Prevalence
- Unknown
- Inheritance
- Autosomal dominant
- Age of onset
- Adult