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Autoimmune polyendocrinopathy type 1

ORPHA:3453· ICD-10 E31.0

Definition

A rare, genetic, disease that manifests in childhood or early adolescence with a combination of chronic mucocutaneous candidiasis, hypoparathyroidism and autoimmune adrenal failure.

Prevalence
1-9 / 100 000
Inheritance
Autosomal recessive
Age of onset
Adolescent, Childhood