Pityriasis rubra pilaris
ORPHA:2897· ICD-10 L44.0
Definition
Pityriasis rubra pilaris is a rare chronic papulosquamous disorder of unknown etiology characterized by small follicular papules, scaly red-orange patches, and palmoplantar hyperkeratosis, which may progress to plaques or erythroderma. Although most of the cases are sporadic and acquired, a familial form of the disease exists.
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Autosomal dominant, Not applicable
- Age of onset
- All ages