Dentinogenesis imperfecta type 3
ORPHA:166265· ICD-10 K00.5
Definition
Dentinogenesis imperfecta type 3 (DGI-3) is a rare, severe form of dentinogenesis imperfecta (DGI) characterized by opalescent primary and permanent teeth, marked attrition, large pulp chambers, multiple pulp exposure and shell teeth radiographically (i.e. teeth which appear hollow due to dentin hypotrophy).
- Prevalence
- Unknown
- Inheritance
- Autosomal dominant
- Age of onset
- Childhood