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Craniofrontonasal dysplasia-Poland anomaly syndrome

ORPHA:1521· ICD-10 Q87.8

Definition

A rare frontonasal dysplasia characterized by craniosynostosis, Poland anomaly, cranio-fronto-nasal dysplasia, and genital and breast anomalies. There have been no further descriptions in the literature since 1994.

Prevalence
<1 / 1 000 000
Inheritance
Unknown
Age of onset
Neonatal