vitalwiki

Neurogenic arthrogryposis multiplex congenita

ORPHA:1143· ICD-10 Q74.3

Definition

A form of arthrogryposis multiplex congenita characterized by congenital immobility of the limbs with fixation of multiple joints and muscle wasting. This condition is secondary to neurogenic muscular atrophy.

Prevalence
1-9 / 100 000
Inheritance
Autosomal recessive
Age of onset
Neonatal