Синдром Кушинга внаслідок ектопічної секреції АКТГ
ORPHA:99889· ICD-10 E24.3· Cushing syndrome due to ectopic ACTH secretion
Визначення(English summary)
A form of adrenocorticotropic hormone (ACTH)-dependent Cushing syndrome, an endogenous Cushing syndrome (CS), characterized by the secretion of ACTH by non-pituitary neuroendocrine tumors (NETs) of various locations and various degrees of histological differentiation and aggressiveness.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- Adult, Elderly