Імунотактоїдна гломерулопатія
ORPHA:97567· ICD-10 N03.6· Immunotactoid glomerulopathy
Визначення(English summary)
Immunotactoid glomerulopathy (ITG) is a very rare condition characterized by glomerular accumulation of microtubules in the mesangium and the glomerular basement membrane, that mainly presents with proteinuria, micro-hematuria, nephrotic syndrome, renal insufficiency and hematologic malignancy. ITG and non-amyloid fibrillary glomerulopathy (non-amyloid FGP, see this term) are often grouped together as pathogenetically related diseases.
- Успадкування
- Not applicable
- Вік початку
- Adult