vitalwiki

Цитофагічний гістіоцитарний панікуліт

ORPHA:94087· ICD-10 M35.8· Cytophagic histiocytic panniculitis

Визначення(English summary)

Cytophagic histiocytic panniculitis (CHP) is a very rare form of panniculitis manifesting as recurrent multiple subcutaneous nodules (which may progressively become ecchymotic and ulcerated), and histologically characterized by lobular panniculitis with lymphocytic and histiocytic infiltration in the subcutaneous adipose tissue.

Поширеність
<1 / 1 000 000
Успадкування
Unknown
Вік початку
Adult