Цитофагічний гістіоцитарний панікуліт
ORPHA:94087· ICD-10 M35.8· Cytophagic histiocytic panniculitis
Визначення(English summary)
Cytophagic histiocytic panniculitis (CHP) is a very rare form of panniculitis manifesting as recurrent multiple subcutaneous nodules (which may progressively become ecchymotic and ulcerated), and histologically characterized by lobular panniculitis with lymphocytic and histiocytic infiltration in the subcutaneous adipose tissue.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Unknown
- Вік початку
- Adult