vitalwiki

Хвороба важких ланцюгів

ORPHA:86864· ICD-10 C88.2· Heavy chain disease

Визначення(English summary)

Heavy-chain diseases (HCDs) are rare monoclonal lymphoplasma-cell proliferative disorders involving B cells and are characterized by the synthesis of truncated heavy chains without associated light chains.

Поширеність
Unknown
Вік початку
Adult