Хвороба важких ланцюгів
ORPHA:86864· ICD-10 C88.2· Heavy chain disease
Визначення(English summary)
Heavy-chain diseases (HCDs) are rare monoclonal lymphoplasma-cell proliferative disorders involving B cells and are characterized by the synthesis of truncated heavy chains without associated light chains.
- Поширеність
- Unknown
- Вік початку
- Adult