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Амілоїдоз АА

ORPHA:85445· ICD-10 E85.3· AA amyloidosis

Визначення(English summary)

A rare amyloidosis that complicates chronic inflammatory disorders and is characterized by the aggregation and deposition of amyloid fibrils composed of serum amyloid A protein, an acute phase reactant. The kidney is involved in virtually all patients and dominates the clinical picture. Other frequently involved sites are the liver, the spleen, suprarenal gland, gut and less frequently the heart.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adolescent, Adult, Childhood