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Хвороба Аддісона

ORPHA:85138· ICD-10 E27.1· Addison disease

Визначення(English summary)

A chronic and rare endocrine disorder due to autoimmune destruction of the adrenal cortex and resulting in a glucocorticoid and mineralocorticoid deficiency. Properly speaking, it designates autoimmune adrenalitis, but it is a term commonly used to describe any form of chronic primary adrenal insufficiency (CPAI).

Поширеність
1-5 / 10 000
Успадкування
Not applicable
Вік початку
All ages