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ORPHA:801· Scleroderma

Визначення(English summary)

Scleroderma is a rare autoimmune connective tissue disorder characterized by abnormal hardening of the skin and, sometimes, other organs. It is classified into two main forms: localized scleroderma and systemic sclerosis (SSc), the latter comprising three subsets; diffuse cutaneous SSc (dcSSc), limited cutaneous SSc (lcSSc) and limited SSc (lSSc).

Поширеність
1-9 / 100 000
Успадкування
Not applicable
Вік початку
All ages