Червоний вовчак
ORPHA:79480· ICD-10 L10.4· Pemphigus erythematosus
Визначення(English summary)
A rare superficial pemphigus disease characterized clinically by well-demarcated, localized, erythematous, scaly, hyperkeratotic, crusted plaques, with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp, and less frequently the extremities, with a photoexposed distribution). Histologically, granular deposits along the dermal-epidermal junction, in addition to intercellular deposition in the upper epidermis, are observed.
- Вік початку
- Adolescent, Adult, Childhood